{"id":832,"date":"2020-12-22T02:25:37","date_gmt":"2020-12-22T00:25:37","guid":{"rendered":"https:\/\/rijetke-bolesti.com\/?page_id=832"},"modified":"2021-03-26T16:33:23","modified_gmt":"2021-03-26T14:33:23","slug":"meneksov-sindrom","status":"publish","type":"page","link":"https:\/\/rijetke-bolesti.com\/en\/rijetke-bolesti\/biblioteka\/meneksov-sindrom\/","title":{"rendered":"Menkesov sindrom"},"content":{"rendered":"<h2 class=\"wp-block-heading\">Menkesov sindrom<\/h2>\n\n\n\n<p><strong>Poznat i kao sindrom kovr\u010dave, nera\u0161\u010de\u0161ljive kose<\/strong><\/p>\n\n\n\n<p>Menkesova bolest nasljedna je, uro\u0111ena metaboli\u010dka bolest uzrokovana poreme\u0107enim unosom i prijenosom bakra u tijelu. Bolest je naziv dobila po pedijatru Johnu Hansu Menkesu koji ju je opisao 1962. godine. Bolest se naziva i \u201esindromom kovr\u010dave, nera\u0161\u010de\u0161ljive kose\u201c zbog posebnog izgleda i strukture kose. Genetska promjena koja uzrokuje bolest nalazi se na X kromosomu, a zahva\u0107a gotovo samo dje\u010dake. Bolest se naj\u010de\u0161\u0107e pojavljuje u dobi od 2-3 mjeseca i to pojavom nezadovoljstva, letargije, epilepti\u010dnih napadaja i drugih neurolo\u0161kih simptoma. Najpoznatiji (klasi\u010dni) oblik bolesti povezan je s te\u0161kim i progresivnim o\u0161te\u0107enjima mozga, \u010desto i plu\u0107a, u ranom djetinjstvu. Opisani su i bla\u017ei oblici bolesti.<\/p>\n\n\n\n<div class=\"wp-block-file\"><a href=\"https:\/\/rijetke-bolesti.com\/wp-content\/uploads\/2020\/12\/dijagnoze_2.pdf\">Meneksov sindrom<\/a><a href=\"https:\/\/rijetke-bolesti.com\/wp-content\/uploads\/2020\/12\/dijagnoze_2.pdf\" class=\"wp-block-file__button\" download>Download<\/a><\/div>","protected":false},"excerpt":{"rendered":"<p>Menkesov sindrom Poznat i kao sindrom kovr\u010dave, nera\u0161\u010de\u0161ljive kose Menkesova bolest nasljedna je, uro\u0111ena metaboli\u010dka bolest uzrokovana poreme\u0107enim unosom i prijenosom bakra u tijelu. Bolest je naziv dobila po pedijatru Johnu Hansu Menkesu koji ju je opisao 1962. godine. Bolest se naziva i \u201esindromom kovr\u010dave,&#8230;<\/p>","protected":false},"author":2,"featured_media":0,"parent":666,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","meta":{"content-type":"","footnotes":""},"class_list":["post-832","page","type-page","status-publish","hentry"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v26.0 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Menkesov sindrom - Hrvatski savez za rijetke bolesti<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/rijetke-bolesti.com\/en\/rijetke-bolesti\/biblioteka\/meneksov-sindrom\/\" \/>\n<meta property=\"og:locale\" content=\"en_GB\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Menkesov sindrom - Hrvatski savez za rijetke bolesti\" \/>\n<meta property=\"og:description\" content=\"Menkesov sindrom Poznat i kao sindrom kovr\u010dave, nera\u0161\u010de\u0161ljive kose Menkesova bolest nasljedna je, uro\u0111ena metaboli\u010dka bolest uzrokovana poreme\u0107enim unosom i prijenosom bakra u tijelu. Bolest je naziv dobila po pedijatru Johnu Hansu Menkesu koji ju je opisao 1962. godine. Bolest se naziva i \u201esindromom kovr\u010dave,...\" \/>\n<meta property=\"og:url\" content=\"https:\/\/rijetke-bolesti.com\/en\/rijetke-bolesti\/biblioteka\/meneksov-sindrom\/\" \/>\n<meta property=\"og:site_name\" content=\"Hrvatski savez za rijetke bolesti\" \/>\n<meta property=\"article:modified_time\" content=\"2021-03-26T14:33:23+00:00\" \/>\n<meta name=\"twitter:card\" content=\"summary_large_image\" \/>\n<meta name=\"twitter:label1\" content=\"Estimated reading time\" \/>\n\t<meta name=\"twitter:data1\" content=\"1 minute\" \/>\n<script type=\"application\/ld+json\" class=\"yoast-schema-graph\">{\"@context\":\"https:\/\/schema.org\",\"@graph\":[{\"@type\":\"WebPage\",\"@id\":\"https:\/\/rijetke-bolesti.com\/rijetke-bolesti\/biblioteka\/meneksov-sindrom\/\",\"url\":\"https:\/\/rijetke-bolesti.com\/rijetke-bolesti\/biblioteka\/meneksov-sindrom\/\",\"name\":\"Menkesov sindrom - Hrvatski savez za rijetke bolesti\",\"isPartOf\":{\"@id\":\"https:\/\/rijetke-bolesti.com\/#website\"},\"datePublished\":\"2020-12-22T00:25:37+00:00\",\"dateModified\":\"2021-03-26T14:33:23+00:00\",\"breadcrumb\":{\"@id\":\"https:\/\/rijetke-bolesti.com\/rijetke-bolesti\/biblioteka\/meneksov-sindrom\/#breadcrumb\"},\"inLanguage\":\"en-GB\",\"potentialAction\":[{\"@type\":\"ReadAction\",\"target\":[\"https:\/\/rijetke-bolesti.com\/rijetke-bolesti\/biblioteka\/meneksov-sindrom\/\"]}]},{\"@type\":\"BreadcrumbList\",\"@id\":\"https:\/\/rijetke-bolesti.com\/rijetke-bolesti\/biblioteka\/meneksov-sindrom\/#breadcrumb\",\"itemListElement\":[{\"@type\":\"ListItem\",\"position\":1,\"name\":\"Home\",\"item\":\"https:\/\/rijetke-bolesti.com\/\"},{\"@type\":\"ListItem\",\"position\":2,\"name\":\"Rijetke bolesti\",\"item\":\"https:\/\/rijetke-bolesti.com\/rijetke-bolesti\/\"},{\"@type\":\"ListItem\",\"position\":3,\"name\":\"Rijetka biblioteka\",\"item\":\"https:\/\/rijetke-bolesti.com\/rijetke-bolesti\/biblioteka\/\"},{\"@type\":\"ListItem\",\"position\":4,\"name\":\"Menkesov sindrom\"}]},{\"@type\":\"WebSite\",\"@id\":\"https:\/\/rijetke-bolesti.com\/#website\",\"url\":\"https:\/\/rijetke-bolesti.com\/\",\"name\":\"Hrvatski savez za rijetke bolesti\",\"description\":\"Za\u0161tita i unapre\u0111enje kvalitete \u017eivota osoba oboljelih\u00a0 od rijetkih bolesti\",\"potentialAction\":[{\"@type\":\"SearchAction\",\"target\":{\"@type\":\"EntryPoint\",\"urlTemplate\":\"https:\/\/rijetke-bolesti.com\/?s={search_term_string}\"},\"query-input\":{\"@type\":\"PropertyValueSpecification\",\"valueRequired\":true,\"valueName\":\"search_term_string\"}}],\"inLanguage\":\"en-GB\"}]}<\/script>\n<!-- \/ Yoast SEO plugin. -->","yoast_head_json":{"title":"Menkesov sindrom - Hrvatski savez za rijetke bolesti","robots":{"index":"index","follow":"follow","max-snippet":"max-snippet:-1","max-image-preview":"max-image-preview:large","max-video-preview":"max-video-preview:-1"},"canonical":"https:\/\/rijetke-bolesti.com\/en\/rijetke-bolesti\/biblioteka\/meneksov-sindrom\/","og_locale":"en_GB","og_type":"article","og_title":"Menkesov sindrom - Hrvatski savez za rijetke bolesti","og_description":"Menkesov sindrom Poznat i kao sindrom kovr\u010dave, nera\u0161\u010de\u0161ljive kose Menkesova bolest nasljedna je, uro\u0111ena metaboli\u010dka bolest uzrokovana poreme\u0107enim unosom i prijenosom bakra u tijelu. Bolest je naziv dobila po pedijatru Johnu Hansu Menkesu koji ju je opisao 1962. godine. 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