{"id":1414,"date":"2021-03-26T11:02:14","date_gmt":"2021-03-26T09:02:14","guid":{"rendered":"https:\/\/rijetke-bolesti.com\/?page_id=1414"},"modified":"2021-03-26T16:51:00","modified_gmt":"2021-03-26T14:51:00","slug":"osteogenesis-imperfecta","status":"publish","type":"page","link":"https:\/\/rijetke-bolesti.com\/en\/rijetke-bolesti\/biblioteka\/osteogenesis-imperfecta\/","title":{"rendered":"Osteogenesis imperfecta"},"content":{"rendered":"<p>Osteogenesis Imperfecta (OI) skupina je rijetkih poreme\u0107aja koji zahva\u0107aju vezivno tkivo, a karakteriziraju ih izuzetno krhke kosti koje se lako lome (lomljive kosti), \u010desto bez o\u010ditog razloga. Specifi\u010dni simptomi i fizi\u010dki nalazi povezani s OI-jem uvelike se razlikuju od slu\u010daja do slu\u010daja.<br>Ozbiljnost OI-ja tako\u0111er se uvelike razlikuje, \u010dak i me\u0111u osobama iz iste obitelji. OI mo\u017ee biti blagi poreme\u0107aj ili mo\u017ee rezultirati ozbiljnim komplikacijama. Utvr\u0111ene su <em>\u010detiri glavne vrste<\/em> OI-ja. OI tipa I<br>naj\u010de\u0161\u0107i je i najbla\u017ei oblik poreme\u0107aja. OI tipa II najte\u017ei je oblik. U ve\u0107ini slu\u010dajeva, razli\u010diti oblici. Osteogenesis Imperfecte naslje\u0111uju se kao autosomno dominantne osobine.<\/p>\n\n\n\n<p><em>Osteogenesis tipa I<\/em> naj\u010de\u0161\u0107i je i obi\u010dno najbla\u017ei oblik ove bolesti. U ve\u0107ini slu\u010dajeva karakteriziraju ga vi\u0161estruki prijelomi kostiju koji se obi\u010dno javljaju tijekom djetinjstva kroz pubertet. Prijelomi obi\u010dno zapo\u010dinju kada oboljelo dijete po\u010dne hodati; prijelomi kod novoro\u0111en\u010dadi su rijetki.<\/p>\n\n\n\n<p><em>Osteogenesis tipa II<\/em> najte\u017ei je oblik bolesti Osteogenesis Imperfecta. Oboljela dojen\u010dad \u010desto ima komplikacije opasne po \u017eivot pri ili ubrzo nakon ro\u0111enja. Dojen\u010dad s OI-jem tipa II ima malu poro\u0111ajnu te\u017einu,<br>abnormalno kratke ruke i noge (udove) i plavi\u010dastu boju bjeloo\u010dnica (plava bjeloo\u010dnica). Osim toga, oboljela novoro\u0111en\u010dad mo\u017ee imati izuzetno krhke kosti i brojne prijelome prisutne pri ro\u0111enju. Rebra i duge kosti nogu oboljele dojen\u010dadi \u010desto su malformirane.<\/p>\n\n\n\n<p><em>Osteogenesis tipa III <\/em>karakteriziraju izuzetno krhke kosti, vi\u0161estruki prijelomi i malformirane kosti. Pri ro\u0111enju su \u010desto prisutni vi\u0161estruki prijelomi. Prijelomi i malformacije razli\u010ditih kostiju (naj\u010de\u0161\u0107e rebara i dugih<br>kostiju) mogu se pogor\u0161avati (progresivne malformacije) kako oboljela novoro\u0111en\u010dad i djeca stare.<\/p>\n\n\n\n<p><em>Osteogenesis tipa IV <\/em> imaju krhke kosti koje se \u010desto lako lome. Prijelomi su \u010de\u0161\u0107i prije puberteta. Oboljele osobe imaju blagu do umjerenu malformaciju kostiju i obi\u010dno su ni\u017ee od prosjeka. Oboljele osobe mogu razviti zakrivljenje kralje\u017enice bo\u010dno ili unatrag (skolioza i kifoza).<\/p>\n\n\n\n<div class=\"wp-block-file\"><a href=\"https:\/\/rijetke-bolesti.com\/wp-content\/uploads\/2021\/03\/dijagnoze_17.pdf\">Osteogenesis Imperfecta (OI)<\/a><a href=\"https:\/\/rijetke-bolesti.com\/wp-content\/uploads\/2021\/03\/dijagnoze_17.pdf\" class=\"wp-block-file__button\" download>Download<\/a><\/div>","protected":false},"excerpt":{"rendered":"<p>Osteogenesis Imperfecta (OI) skupina je rijetkih poreme\u0107aja koji zahva\u0107aju vezivno tkivo, a karakteriziraju ih izuzetno krhke kosti koje se lako lome (lomljive kosti), \u010desto bez o\u010ditog razloga. Specifi\u010dni simptomi i fizi\u010dki nalazi povezani s OI-jem uvelike se razlikuju od slu\u010daja do slu\u010daja.Ozbiljnost OI-ja tako\u0111er se&#8230;<\/p>","protected":false},"author":2,"featured_media":0,"parent":666,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","meta":{"content-type":"","footnotes":""},"class_list":["post-1414","page","type-page","status-publish","hentry"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v26.0 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Osteogenesis imperfecta - Hrvatski savez za rijetke bolesti<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/rijetke-bolesti.com\/en\/rijetke-bolesti\/biblioteka\/osteogenesis-imperfecta\/\" \/>\n<meta property=\"og:locale\" content=\"en_GB\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Osteogenesis imperfecta - Hrvatski savez za rijetke bolesti\" \/>\n<meta property=\"og:description\" content=\"Osteogenesis Imperfecta (OI) skupina je rijetkih poreme\u0107aja koji zahva\u0107aju vezivno tkivo, a karakteriziraju ih izuzetno krhke kosti koje se lako lome (lomljive kosti), \u010desto bez o\u010ditog razloga. Specifi\u010dni simptomi i fizi\u010dki nalazi povezani s OI-jem uvelike se razlikuju od slu\u010daja do slu\u010daja.Ozbiljnost OI-ja tako\u0111er se...\" \/>\n<meta property=\"og:url\" content=\"https:\/\/rijetke-bolesti.com\/en\/rijetke-bolesti\/biblioteka\/osteogenesis-imperfecta\/\" \/>\n<meta property=\"og:site_name\" content=\"Hrvatski savez za rijetke bolesti\" \/>\n<meta property=\"article:modified_time\" content=\"2021-03-26T14:51:00+00:00\" \/>\n<meta name=\"twitter:card\" content=\"summary_large_image\" \/>\n<meta name=\"twitter:label1\" content=\"Estimated reading time\" \/>\n\t<meta name=\"twitter:data1\" content=\"2 minutes\" \/>\n<script type=\"application\/ld+json\" class=\"yoast-schema-graph\">{\"@context\":\"https:\/\/schema.org\",\"@graph\":[{\"@type\":\"WebPage\",\"@id\":\"https:\/\/rijetke-bolesti.com\/rijetke-bolesti\/biblioteka\/osteogenesis-imperfecta\/\",\"url\":\"https:\/\/rijetke-bolesti.com\/rijetke-bolesti\/biblioteka\/osteogenesis-imperfecta\/\",\"name\":\"Osteogenesis imperfecta - Hrvatski savez za rijetke bolesti\",\"isPartOf\":{\"@id\":\"https:\/\/rijetke-bolesti.com\/#website\"},\"datePublished\":\"2021-03-26T09:02:14+00:00\",\"dateModified\":\"2021-03-26T14:51:00+00:00\",\"breadcrumb\":{\"@id\":\"https:\/\/rijetke-bolesti.com\/rijetke-bolesti\/biblioteka\/osteogenesis-imperfecta\/#breadcrumb\"},\"inLanguage\":\"en-GB\",\"potentialAction\":[{\"@type\":\"ReadAction\",\"target\":[\"https:\/\/rijetke-bolesti.com\/rijetke-bolesti\/biblioteka\/osteogenesis-imperfecta\/\"]}]},{\"@type\":\"BreadcrumbList\",\"@id\":\"https:\/\/rijetke-bolesti.com\/rijetke-bolesti\/biblioteka\/osteogenesis-imperfecta\/#breadcrumb\",\"itemListElement\":[{\"@type\":\"ListItem\",\"position\":1,\"name\":\"Home\",\"item\":\"https:\/\/rijetke-bolesti.com\/\"},{\"@type\":\"ListItem\",\"position\":2,\"name\":\"Rijetke bolesti\",\"item\":\"https:\/\/rijetke-bolesti.com\/rijetke-bolesti\/\"},{\"@type\":\"ListItem\",\"position\":3,\"name\":\"Rijetka biblioteka\",\"item\":\"https:\/\/rijetke-bolesti.com\/rijetke-bolesti\/biblioteka\/\"},{\"@type\":\"ListItem\",\"position\":4,\"name\":\"Osteogenesis imperfecta\"}]},{\"@type\":\"WebSite\",\"@id\":\"https:\/\/rijetke-bolesti.com\/#website\",\"url\":\"https:\/\/rijetke-bolesti.com\/\",\"name\":\"Hrvatski savez za rijetke bolesti\",\"description\":\"Za\u0161tita i unapre\u0111enje kvalitete \u017eivota osoba oboljelih\u00a0 od rijetkih bolesti\",\"potentialAction\":[{\"@type\":\"SearchAction\",\"target\":{\"@type\":\"EntryPoint\",\"urlTemplate\":\"https:\/\/rijetke-bolesti.com\/?s={search_term_string}\"},\"query-input\":{\"@type\":\"PropertyValueSpecification\",\"valueRequired\":true,\"valueName\":\"search_term_string\"}}],\"inLanguage\":\"en-GB\"}]}<\/script>\n<!-- \/ Yoast SEO plugin. -->","yoast_head_json":{"title":"Osteogenesis imperfecta - Hrvatski savez za rijetke bolesti","robots":{"index":"index","follow":"follow","max-snippet":"max-snippet:-1","max-image-preview":"max-image-preview:large","max-video-preview":"max-video-preview:-1"},"canonical":"https:\/\/rijetke-bolesti.com\/en\/rijetke-bolesti\/biblioteka\/osteogenesis-imperfecta\/","og_locale":"en_GB","og_type":"article","og_title":"Osteogenesis imperfecta - Hrvatski savez za rijetke bolesti","og_description":"Osteogenesis Imperfecta (OI) skupina je rijetkih poreme\u0107aja koji zahva\u0107aju vezivno tkivo, a karakteriziraju ih izuzetno krhke kosti koje se lako lome (lomljive kosti), \u010desto bez o\u010ditog razloga. 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