{"id":1408,"date":"2021-03-26T11:00:09","date_gmt":"2021-03-26T09:00:09","guid":{"rendered":"https:\/\/rijetke-bolesti.com\/?page_id=1408"},"modified":"2021-03-26T16:53:57","modified_gmt":"2021-03-26T14:53:57","slug":"hemofilija","status":"publish","type":"page","link":"https:\/\/rijetke-bolesti.com\/en\/rijetke-bolesti\/biblioteka\/hemofilija\/","title":{"rendered":"Hemofilija"},"content":{"rendered":"<p>Hemofilija A, tako\u0111er poznata i kao klasi\u010dna hemofilija, genetski je poreme\u0107aj krvarenja uzrokovan nedovoljnom razinom krvnog proteina zvanog faktor VIII. Faktor VIII faktor je zgru\u0161avanja.<\/p>\n\n\n\n<p><em>Hemofiliju A<\/em> uzrokuju poreme\u0107aji ili promjene (mutacije) gena F8 na X kromosomu. Ta se mutacija mo\u017ee naslijediti ili se pojaviti slu\u010dajno, bez povijesti poreme\u0107aja u obitelji (spontano). Hemofilija A uglavnom se javlja kod mu\u0161karaca, ali neke \u017eene koje nose gen mogu imati blage ili, rijetko, te\u017ee simptome krvarenja. Iako ne postoji lijek za hemofiliju, razvijene su u\u010dinkovite terapije, te ve\u0107ina oboljelih osoba mo\u017ee voditi ispunjen, produktivan \u017eivot uz odgovaraju\u0107e lije\u010denje i njegu.<\/p>\n\n\n\n<p><em>Hemofilija B<\/em> rijedak je genetski poreme\u0107aj krvarenja kod kojeg oboljele osobe nemaju dovoljno razine krvnog proteina koji se naziva faktor IX. Osobe s hemofilijom B ne krvare br\u017ee od osoba koje ne boluju od te bolesti, ve\u0107 krvare du\u017ee.<\/p>\n\n\n\n<div class=\"wp-block-file\"><a href=\"https:\/\/rijetke-bolesti.com\/wp-content\/uploads\/2021\/03\/dijagnoze_15.pdf\">Hemofilija <\/a><a href=\"https:\/\/rijetke-bolesti.com\/wp-content\/uploads\/2021\/03\/dijagnoze_15.pdf\" class=\"wp-block-file__button\" download>Download<\/a><\/div>\n\n\n\n<p><\/p>","protected":false},"excerpt":{"rendered":"<p>Hemofilija A, tako\u0111er poznata i kao klasi\u010dna hemofilija, genetski je poreme\u0107aj krvarenja uzrokovan nedovoljnom razinom krvnog proteina zvanog faktor VIII. Faktor VIII faktor je zgru\u0161avanja. Hemofiliju A uzrokuju poreme\u0107aji ili promjene (mutacije) gena F8 na X kromosomu. Ta se mutacija mo\u017ee naslijediti ili se pojaviti&#8230;<\/p>","protected":false},"author":2,"featured_media":0,"parent":666,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","meta":{"content-type":"","footnotes":""},"class_list":["post-1408","page","type-page","status-publish","hentry"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v26.0 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Hemofilija - Hrvatski savez za rijetke bolesti<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/rijetke-bolesti.com\/en\/rijetke-bolesti\/biblioteka\/hemofilija\/\" \/>\n<meta property=\"og:locale\" content=\"en_GB\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Hemofilija - Hrvatski savez za rijetke bolesti\" \/>\n<meta property=\"og:description\" content=\"Hemofilija A, tako\u0111er poznata i kao klasi\u010dna hemofilija, genetski je poreme\u0107aj krvarenja uzrokovan nedovoljnom razinom krvnog proteina zvanog faktor VIII. Faktor VIII faktor je zgru\u0161avanja. Hemofiliju A uzrokuju poreme\u0107aji ili promjene (mutacije) gena F8 na X kromosomu. Ta se mutacija mo\u017ee naslijediti ili se pojaviti...\" \/>\n<meta property=\"og:url\" content=\"https:\/\/rijetke-bolesti.com\/en\/rijetke-bolesti\/biblioteka\/hemofilija\/\" \/>\n<meta property=\"og:site_name\" content=\"Hrvatski savez za rijetke bolesti\" \/>\n<meta property=\"article:modified_time\" content=\"2021-03-26T14:53:57+00:00\" \/>\n<meta name=\"twitter:card\" content=\"summary_large_image\" \/>\n<meta name=\"twitter:label1\" content=\"Estimated reading time\" \/>\n\t<meta name=\"twitter:data1\" content=\"1 minute\" \/>\n<script type=\"application\/ld+json\" class=\"yoast-schema-graph\">{\"@context\":\"https:\/\/schema.org\",\"@graph\":[{\"@type\":\"WebPage\",\"@id\":\"https:\/\/rijetke-bolesti.com\/rijetke-bolesti\/biblioteka\/hemofilija\/\",\"url\":\"https:\/\/rijetke-bolesti.com\/rijetke-bolesti\/biblioteka\/hemofilija\/\",\"name\":\"Hemofilija - Hrvatski savez za rijetke bolesti\",\"isPartOf\":{\"@id\":\"https:\/\/rijetke-bolesti.com\/#website\"},\"datePublished\":\"2021-03-26T09:00:09+00:00\",\"dateModified\":\"2021-03-26T14:53:57+00:00\",\"breadcrumb\":{\"@id\":\"https:\/\/rijetke-bolesti.com\/rijetke-bolesti\/biblioteka\/hemofilija\/#breadcrumb\"},\"inLanguage\":\"en-GB\",\"potentialAction\":[{\"@type\":\"ReadAction\",\"target\":[\"https:\/\/rijetke-bolesti.com\/rijetke-bolesti\/biblioteka\/hemofilija\/\"]}]},{\"@type\":\"BreadcrumbList\",\"@id\":\"https:\/\/rijetke-bolesti.com\/rijetke-bolesti\/biblioteka\/hemofilija\/#breadcrumb\",\"itemListElement\":[{\"@type\":\"ListItem\",\"position\":1,\"name\":\"Home\",\"item\":\"https:\/\/rijetke-bolesti.com\/\"},{\"@type\":\"ListItem\",\"position\":2,\"name\":\"Rijetke bolesti\",\"item\":\"https:\/\/rijetke-bolesti.com\/rijetke-bolesti\/\"},{\"@type\":\"ListItem\",\"position\":3,\"name\":\"Rijetka biblioteka\",\"item\":\"https:\/\/rijetke-bolesti.com\/rijetke-bolesti\/biblioteka\/\"},{\"@type\":\"ListItem\",\"position\":4,\"name\":\"Hemofilija\"}]},{\"@type\":\"WebSite\",\"@id\":\"https:\/\/rijetke-bolesti.com\/#website\",\"url\":\"https:\/\/rijetke-bolesti.com\/\",\"name\":\"Hrvatski savez za rijetke bolesti\",\"description\":\"Za\u0161tita i unapre\u0111enje kvalitete \u017eivota osoba oboljelih\u00a0 od rijetkih bolesti\",\"potentialAction\":[{\"@type\":\"SearchAction\",\"target\":{\"@type\":\"EntryPoint\",\"urlTemplate\":\"https:\/\/rijetke-bolesti.com\/?s={search_term_string}\"},\"query-input\":{\"@type\":\"PropertyValueSpecification\",\"valueRequired\":true,\"valueName\":\"search_term_string\"}}],\"inLanguage\":\"en-GB\"}]}<\/script>\n<!-- \/ Yoast SEO plugin. -->","yoast_head_json":{"title":"Hemofilija - Hrvatski savez za rijetke bolesti","robots":{"index":"index","follow":"follow","max-snippet":"max-snippet:-1","max-image-preview":"max-image-preview:large","max-video-preview":"max-video-preview:-1"},"canonical":"https:\/\/rijetke-bolesti.com\/en\/rijetke-bolesti\/biblioteka\/hemofilija\/","og_locale":"en_GB","og_type":"article","og_title":"Hemofilija - Hrvatski savez za rijetke bolesti","og_description":"Hemofilija A, tako\u0111er poznata i kao klasi\u010dna hemofilija, genetski je poreme\u0107aj krvarenja uzrokovan nedovoljnom razinom krvnog proteina zvanog faktor VIII. Faktor VIII faktor je zgru\u0161avanja. Hemofiliju A uzrokuju poreme\u0107aji ili promjene (mutacije) gena F8 na X kromosomu. 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