{"id":1402,"date":"2021-03-26T10:58:32","date_gmt":"2021-03-26T08:58:32","guid":{"rendered":"https:\/\/rijetke-bolesti.com\/?page_id=1402"},"modified":"2021-03-26T16:45:46","modified_gmt":"2021-03-26T14:45:46","slug":"cisticna-fibroza","status":"publish","type":"page","link":"https:\/\/rijetke-bolesti.com\/en\/rijetke-bolesti\/biblioteka\/cisticna-fibroza\/","title":{"rendered":"Cisti\u010dna fibroza"},"content":{"rendered":"<p>Cisti\u010dna fibroza genetski je poreme\u0107aj koji \u010desto utje\u010de na vi\u0161e organskih sustava tijela. Cisti\u010dnu fibrozu karakteriziraju abnormalnosti koje zahva\u0107aju odre\u0111ene \u017elijezde (egzokrine) u tijelu, posebno one koje<br>stvaraju sluz. Tako\u0111er mogu biti zahva\u0107ene slinovnice i znojnice. Egzokrine \u017elijezde lu\u010de tvari kroz kanale, bilo iznutra (npr. \u017elijezde u plu\u0107ima) ili izvana (npr. znojne \u017elijezde). Kod cisti\u010dne fibroze, te izlu\u010devine postaju neobi\u010dno guste i mogu za\u010depiti vitalna podru\u010dja tijela uzrokuju\u0107i upalu, opstrukciju i infekciju. Simptomi cisti\u010dne fibroze mogu se uvelike razlikovati po broju i te\u017eini od osobe do osobe.<br>Uobi\u010dajeni simptomi uklju\u010duju abnormalnosti disanja (respiratorne), uklju\u010duju\u0107i trajni ka\u0161alj, ote\u017eano disanje i infekcije plu\u0107a, za\u010depljenje gu\u0161tera\u010de, \u0161to spre\u010dava probavne enzime da do\u0111u do crijeva kako bi<br>pomogli razgradnji hrane, a mo\u017ee rezultirati lo\u0161im rastom i lo\u0161om prehranom, i za\u010depljenje crijeva.<br>Cisti\u010dna fibroza polako napreduje i \u010desto uzrokuje kroni\u010dno o\u0161te\u0107enje plu\u0107a, \u0161to na kraju rezultira komplikacijama opasnim po \u017eivot.<\/p>\n\n\n\n<p>Cisti\u010dna fibroza \u010desto je vidljiva nedugo nakon ro\u0111enja, ali prije uvo\u0111enja novoro\u0111ena\u010dkog probira, u slu\u010dajevima kada simptomi nisu bili ozbiljni, CF se ponekad otkrivao tek godinama kasnije, a u rijetkim slu\u010dajevima \u010dak i tek u odrasloj dobi. Ve\u0107ina slu\u010dajeva dijagnosticiranih u odrasloj dobi.<\/p>\n\n\n\n<p><\/p>\n\n\n\n\n\n<div class=\"wp-block-file\"><a href=\"https:\/\/rijetke-bolesti.com\/wp-content\/uploads\/2021\/03\/dijagnoze_13.pdf\">Cisti\u010dna fibroza<\/a><a href=\"https:\/\/rijetke-bolesti.com\/wp-content\/uploads\/2021\/03\/dijagnoze_13.pdf\" class=\"wp-block-file__button\" download>Download<\/a><\/div>","protected":false},"excerpt":{"rendered":"<p>Cisti\u010dna fibroza genetski je poreme\u0107aj koji \u010desto utje\u010de na vi\u0161e organskih sustava tijela. Cisti\u010dnu fibrozu karakteriziraju abnormalnosti koje zahva\u0107aju odre\u0111ene \u017elijezde (egzokrine) u tijelu, posebno one kojestvaraju sluz. Tako\u0111er mogu biti zahva\u0107ene slinovnice i znojnice. Egzokrine \u017elijezde lu\u010de tvari kroz kanale, bilo iznutra (npr. \u017elijezde&#8230;<\/p>","protected":false},"author":2,"featured_media":0,"parent":666,"menu_order":0,"comment_status":"closed","ping_status":"closed","template":"","meta":{"content-type":"","footnotes":""},"class_list":["post-1402","page","type-page","status-publish","hentry"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v26.0 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Cisti\u010dna fibroza - Hrvatski savez za rijetke bolesti<\/title>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/rijetke-bolesti.com\/en\/rijetke-bolesti\/biblioteka\/cisticna-fibroza\/\" \/>\n<meta property=\"og:locale\" content=\"en_GB\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Cisti\u010dna fibroza - Hrvatski savez za rijetke bolesti\" \/>\n<meta property=\"og:description\" content=\"Cisti\u010dna fibroza genetski je poreme\u0107aj koji \u010desto utje\u010de na vi\u0161e organskih sustava tijela. Cisti\u010dnu fibrozu karakteriziraju abnormalnosti koje zahva\u0107aju odre\u0111ene \u017elijezde (egzokrine) u tijelu, posebno one kojestvaraju sluz. Tako\u0111er mogu biti zahva\u0107ene slinovnice i znojnice. 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Cisti\u010dnu fibrozu karakteriziraju abnormalnosti koje zahva\u0107aju odre\u0111ene \u017elijezde (egzokrine) u tijelu, posebno one kojestvaraju sluz. Tako\u0111er mogu biti zahva\u0107ene slinovnice i znojnice. 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